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障害者対策総合研究事業(神経・筋疾患分野)

(○:委員長)

葛原 茂樹 鈴鹿医療科学大学保健衛生学部医療福祉学科教授
神経変性疾患、痴呆性疾患、医原性神経疾患、脳血管障害
Ishiura H, Takahashi Y, Mitsui J, Yoshida S, Kihira T, Kokubo Y, Kuzuhara S, Ranum LP, Tamaoki T, Ichikawa Y, Date H, Goto J, Tsuji S.
C9ORF72 Repeat Expansion in Amyotrophic Lateral Sclerosis in the Kii Peninsula of JapanC9ORF72 Repeat Expansion in ALS. Arch Neurol. 2012 Jun 4:1-5.
Kokubo Y, Taniguchi A, Hasegawa M, Hayakawa Y, Morimoto S, Yoneda M, Hirokawa Y, Shiraishi T, Saito Y, Murayama S, Kuzuhara S. α-Synuclein pathology in the amyotrophic lateral sclerosis/parkinsonism dementia complex in the Kii Peninsula, Japan.J Neuropathol Exp Neurol. 2012 Jul;71(7):625-30.
Kuzuhara S, Kokubo Y, Sasaki R, Narita Y, Yabana T, Hasegawa M, Iwatsubo T: Familial amyotrophic lateral sclerosis and parkinsonism-dementia complex of the Kii peninsula of Japan: clinical and neuropathological study and tau analysis. Ann Neurol 49:501-511, 2001
 
篠原 幸人 国家公務員共済組合連合会立川病院 院長
神経内科学
Shinohara Y: Hemorrhagic stroke syndrome: Clinical manifestation of intracerebral and subarachnoid hemorrhage.
In “Handbook of Clinical Neurology, Vol. 93, Chap 28”, ed by Mark Fisher.
Elsevier, Edinburgh. pp577-594, 2009
Shinohara Y, Katayama Y, Uchiyama S, Yamaguchi T, Handa S, Matsuoka K, Ohashi Y, Tanahashi N, Yamamoto H, Genka C, Kitagawa Y, Kusuoka H, Nishimaru K, Tushima M, Koretsune Y, Sawada T, Hamada C, for the CSPS 2 group: Cilostazol for prevention of secondary stroke (CSPS 2): an aspirin-controlled, double-blind, randomised non-inferiority trial.
Lancet Neurol 9: 959-968, 2010
Shinohara Y, Goto S, Doi M, Jensen P: Safety of the novel protease-activated receptor-1 antagonist vorapaxar in Japanese patients with a history of ischemic stroke.
J Stroke Cerebrovasc Dis 21: 318-324, 2012
 
高守 正治 金沢西病院脳神経センター長 金沢大学名誉教授
神経免疫学、神経生理学
Lambert-Eaton myasthenic syndrome: search for alternative autoimmune targets and possible compensatory mechanisms based on presynaptic calcium homeostasis. Takamori M. J Neuroimmunol. 2008 Sept; 201-202: 145-152.
Autoantibodies against TRPC3 and ryanodine receptor in myasthenia gravis. Takamori M. J Neuroimmunol. 2008 Aug; 200(1-2): 142-144.
Autoantibodies against M1 muscarinic acetylcholine receptor in myasthenic disorders. Takamori M, Motomura M, Fukudome T, Yoshikawa H. Eur J Neurol 2007 Nov; 14(11): 1230-1235.
 
田村 晃 富士脳障害研究所附属病院院長
脳神経外科
Kuroiwa T, Miyasaka N, Fengyo Z, Yamada I, Nakane M, Nagaoka T, Tamura A, Ohno K: Experimental ischemic brain edema: morphological and magnetic resonance imaging findings. Neurosurg Focus 2007;22(5):E11(1-8)
Ohwaki K, Yano E, Nagashima H, Hirata M, Nakagomi T, Tamura A. Blood pressure management in acute intracerebral hemorrhage: relationship between elevated blood pressure and hematoma enlargement. Stroke 2004;35(6):1364-1367
Nakatomi H, Kuriu T. Okabe S, Yamamoto S, Hatano O, Kawahara N, Tamura A, Kirino T, Nakafuku M: Regeneration of hippocampal pyramidal neurons after ischemic brain injury by recruitment of endogenous neural progenitors. Cell 2002; 110:429-441
 
西澤 正豊 新潟大学脳研究所神経内科学分野教授
神経内科学
Yanagawa K, Kawachi I, Yokoseki A, Arakawa M, Hasegawa A, Ito Y, Kojima N, Koike R, Tanaka K, Kosaka T, Tan C-F, Toyoshima Y, Kakita A, Tsujita M, Sakimura K, Takahashi H, Nishizawa M: Clinical course and pathological characterization of a limited form of neuromyelitis optica with myelitis: homogeneity of pathogenesis and heterogeneity of treatment response through long-term courses of neuromyelitis optica. Neurology 2009; 73 (20): 1628-1637. PMID: 19917985
Kanazawa M, Shimohata T, Toyoshima Y, Tada M, Kakita A, Morita T, Ozawa T, Takahashi H, Nishizawa M: Cerebellar involvement in progressive supranuclear palsy: a clinicopathological study. Mov Disord 2009; 24 (9): 1312-1318. PMID: 19412943
Shimohata T, Shinoda H, Nakayama H, Ozawa T, Terajima K, Yoshizawa H, Matsuzawa Y, Onodera O, Naruse S, Tanaka K, Takahashi S, Gejyo F, Nishizawa M.: Daytime hypoxemia, sleep-disordered breathing, and laryngopharyngeal findings in multiple system atrophy. Arch Neurol 2007; 64 (6): 856-861, PMID: 17562934
 
御子柴 克彦 理化学研究所グループディレクター
脳神経科学
Futatsugi, A., Nakamura, T., Yamada, M. K.,Ebisui, E., Nakamura, K., Uchida, K., Kitaguchi, T., Takahashi-Iwanaga, H., Noda, T., Aruga, J. & Mikoshiba, K.: IP3 Receptor Types 2 and 3 mediate exocrine secretion underlying energy metabolism Science 309: 2232-2234 (2005)
Higo, T., Hattori, M., Nakamura, T., Natsume, T., Michikawa, T & Mikoshiba,K.:Subtype-specific and ER-lumenal-environment-dependent Regulation of Inositol 1,4,5-Trisphosphate Receptor Type 1 by ERp44. Cell 120: 85-98 (2005)
Higo T, Hamada K, Hisatsune C, Nukina N, Hashikawa T, Hattori M, Nakamura T, Mikoshiba K. Mechanism of ER stress-induced brain damage by IP3 receptor. Neuron 68(5): 865-878 (2010)

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